Abstract:
Background. Moyamoya disease is a cerebrovascular disease that is characterized by bilateral
chronic and progressive stenosis or occlusion of the arteries around the circle of Willis with
development of collateral circulation, of unknown etiology. It has a high incidence in Japan and
Asian population, with fewer cases described in Europe. Similar angiographic findings can be
seen in patients with other medical conditions that are described as Moyamoya syndrome. Main
clinical features include transient ischemic attacks, ischemic strokes, and hemorrhagic strokes.
