Abstract:
Background. Congenital cystic adenomatoid malformation (CCAM) is a rare developmental
abnormality of the lung with an incidence of 1 in 25,000 to 1 in 35,000 pregnancies and
represents 25% of congenital lung malformations and 95% of congenital lung lesions, males and
females being equally affected. It is characterized by multicystic mass arising in the lung
parenchyma from abnormal proliferation of the immature terminal respiratory bronchioles. The
clinical spectrum is wide and ranges from silent incidental lesions to severe congenital
respiratory distress or stillbirths. The diagnosis of CCAM can be made in utero by prenatal
ultrasongraphy and postnatally by imaging radiography and CT. We report a case of a CCAM,
which provoked spontaneous pneumothorax.
