Abstract:
Introduction. The histological ambiguity of the retroperitoneal space is the cause of the large
specter of primitive tumors. Primitive tumors are classified in those with a mesodermal origin,
neurogenic, vestigial, retroperitoneal cysts and various tumors. The neurogenic tumors may have
different origins: ganglion cell (ganglioneuromas, ganglioneuroblastomas, neuroblastomas),
paraganglionic system (paragangliomas, pheochromocytomas) and nerve sheath (schwannomas,
neurofibromas, malignant schwannomas). The neurogenic primitives tumors usually present late
symptoms or become palpable once they have reached a significant size (>10cm). The medical
imaging (USG, CT, IRM) does not distinguish benign and malign tumors, and it does not reveal
the histological origin. The biopsy and the histological examination of the removed tumor remain
the main diagnostic methods.
